Table 1 VCUAM classification[8]
From: Malformations in a cohort of 284 women with Mayer-Rokitansky-Küster-Hauser syndrome (MRKH)
Organ | Stage | Description |
|---|---|---|
Vagina (V) | 0 | Normal |
1a | Partial hymenal atresia | |
1b | Complete hymenal atresia | |
2a | Incomplete septate vagina < 50% | |
2b | Complete septate vagina | |
3 | Stenosis of the introitus | |
4 | Hypoplasia | |
5a | Unilateral atresia | |
5b | Complete atresia | |
S1 | Sinus urogenitalis (deep confluence) | |
S2 | Sinus urogenitalis (middle confluence) | |
S3 | Sinus urogenitalis (high confluence) | |
C | Cloacae | |
+ | Other | |
# | Unknown | |
Cervix (C) | 0 | Normal |
1 | Duplex cervix | |
2a | Unilateral atresia/aplasia | |
2b | Bilateral atresia/aplasia | |
+ | Other | |
# | Unknown | |
Uterus (U) | 0 | Normal |
1a | Arcuate | |
1b | Septate <50% of the uterine cavity | |
1c | Septate >50% of the uterine cavity | |
2 | Bicornate | |
3 | Hypoplastic uterus | |
4a | Unilaterally rudimentary or aplastic | |
4b | Bilaterally rudimentary or aplastic | |
+ | Other | |
# | Unknown | |
Adnexa (A) | 0 | Normal |
1a | Unilateral tubal malformation, ovaries normal | |
1b | Bilateral tubal malformation, ovaries normal | |
2a | Unilateral hypoplasia/gonadal streak (including tubal malformation if appropriate) | |
2b | Bilateral hypoplasia/gonadal streak (including tubal malformation if appropriate) | |
3a | Unilateral aplasia | |
3b | Bilateral aplasia | |
+ | Other | |
# | Unknown | |
Associated malformations (M) | 0 | None |
R | Renal system | |
S | Skeleton | |
C | Cardiac | |
N | Neurologic | |
+ | Other | |
# | Unknown |