Skip to main content

Table 2 VCUAM classification of 284 patients with MRKH syndrome

From: Malformations in a cohort of 284 women with Mayer-Rokitansky-Küster-Hauser syndrome (MRKH)

Vagina

n (%)

Cervix

n (%)

Uterus

n (%)

Adnexa

n (%)

Malformation

n (%)

V5b

284 (100%)

C2b

284 (100%)

U0

0 (0%)

A0

248 (87.3%)

M0

156 (54.9%)

    

U1a

0 (0%)

A1a

1 (0.4%)

MR

53 (18.7%)

    

U1b

0 (0%)

A1b

7 (2.5%)

MS

22 (7.7%)

    

U1c

0 (0%)

A2a

10 (3.5%)

MC

2 (0.7%)

    

U2

0 (0%)

A2b

2 (0.7%)

MN

4 (1.4%)

    

U3

2 (0.7%)

A3a

6 (2.1%)

M+

5 (1.8%)

    

U4a

27 (9.5%)

A3b

0 (0%)

M#

2 (0.7%)

    

U4b

239 (84.2%)

A+

1 (0.4%)

Combinations

 
    

U+

8 (2.8%)

A#

9 (3.2%)

MR+

3 (1.1%)

    

U#

8 (2.8%)

  

MRC

1 (0.4%)

        

MRC+

1 (0.4)

        

MRN

2 (0.7%)

        

MRS

15 (5.3)

        

MRS+

4 (1.4%)

        

MRSC

2 (0.7)

        

MRSN

3 (1.1%)

        

MS+

2 (0.7%)

        

MSC

1 (0.4)

        

MSCN

2 (0.7%)

        

MSN

3 (1.1)

        

MC+

1 (0.4)